Progressive idiopathic lung fibrosis; computed tomography shows usual interstitial pneumonia pattern
Expansion
Idiopathic Pulmonary Fibrosis
Purpose
Diagnosed by clinical plus imaging criteria; median survival approximately 3 years
Clinical Context
Idiopathic pulmonary fibrosis no known cause. High-resolution computed tomography usual interstitial pneumonia pattern shows basal reticular, traction bronchiectasis, honeycombing equals diagnostic. Pulmonary function tests show restrictive pattern, low diffusing capacity for carbon monoxide.
Related Terms
- Usual interstitial pneumonia
- Interstitial lung disease
Key Points
- Idiopathic pulmonary fibrosis high-resolution computed tomography typical usual interstitial pneumonia pattern shows basal-predominant reticular opacities, traction bronchiectasis, honeycombing