Mnemonic

Haemolysis Investigation

A memory aid for the markers of haemolysis.

Expansion

Raised reticulocytes, bilirubin and LDH with low haptoglobin

Expansion

Markers of increased red cell destruction

  • Unconjugated bilirubin raised, giving prehepatic jaundice
  • LDH raised, released from lysed cells
  • Haptoglobin low or absent, consumed by binding free haemoglobin
  • Urinary urobilinogen raised; haemosiderinuria in chronic intravascular haemolysis

Markers of increased production

  • Reticulocytosis, with polychromasia on the film

Then classify

  • Direct antiglobulin (Coombs) test: positive means immune haemolysis, warm (IgG, often idiopathic, lupus, lymphoma, methyldopa) or cold (IgM, Mycoplasma, infectious mononucleosis)
  • Negative Coombs: consider membrane defects (spherocytosis), enzyme defects (G6PD, pyruvate kinase), haemoglobinopathies, mechanical causes (prosthetic valves, microangiopathy), infection (malaria) and paroxysmal nocturnal haemoglobinuria

The blood film is often diagnostic: spherocytes, sickle cells, bite cells and Heinz bodies in G6PD, schistocytes in microangiopathy, and malarial parasites.

Intravascular haemolysis causes haemoglobinuria and profound haptoglobin depletion; extravascular haemolysis in the spleen causes splenomegaly and jaundice.